Calcifying Cystic Odontogenic Tumor with Compound Odontoma

Calcifying cystic odontogenic tumor (CCOT) previously known as calcifying odontogenic cyst (COC) is a relatively rare lesion. It was first reported as a separate pathologic entity by Gorlin et al in 1962 as a likely analog of the cutaneous calcifying epithelioma of Malherbe or pilomatricoma. Because of the diverse clinicohistologic features and the various neoplastic potential, there have been disagreements on the terminology as well as whether to classify CCOTs as a cyst or a neoplasm. CCOT is frequently associated with other lesions, such as odontoma, ameloblastoma and ameloblastic fibroma, and the most common of these is the CCOT-associated odontoma (CCOTaO). CCOTaO tends to occur in the anterior portion of upper jaw and occurs in younger age group as compared to other types. We present a case of CCOTaO in the posterior mandible of a 23-year-old male.